RADIATION-INDUCED SARCOMAS: A SURGICAL CHALLENGE

  • Paula Ferreira Pinto Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal
  • José Carlos Pereira Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal
  • Ana Margarida Correia Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal http://orcid.org/0000-0003-0112-7401
  • Catarina Baía Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal http://orcid.org/0000-0002-0696-5212
  • Mariana Marques Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal
  • José Silva Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal
  • Pedro Martins Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal
  • Lúcio Lara Santos Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal; Experimental Pathology and Therapeutics Group, Portuguese Institute of Oncology, Porto, Portugal http://orcid.org/0000-0002-0521-5655
  • Joaquim Abreu de Sousa Surgical Oncology Department, Portuguese Institute of Oncology, Porto, Portugal http://orcid.org/0000-0002-4988-6987

Abstract


Malignant peripheral nerve sheath tumors (MPNST) are uncommon, biologically challenging soft tissue sarcomas. The definitive treatment of these tumors is extremely challenging. In 50% of cases, these tumors are associated with type I neurofibromatosis, but in some cases, the cause can be previous treatment with radiotherapy. The present article pretends to report a clinical case of a radiation-induced MPNST submitted to surgical treatment.

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References

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Published
2024-01-11
How to Cite
FERREIRA PINTO, Paula et al. RADIATION-INDUCED SARCOMAS: A SURGICAL CHALLENGE. Revista Portuguesa de Cirurgia, [S.l.], n. 56, p. 77-80, jan. 2024. ISSN 2183-1165. Available at: <https://revista.spcir.com/index.php/spcir/article/view/984>. Date accessed: 29 feb. 2024. doi: https://doi.org/10.34635/rpc.984.
Section
Clinical Case