Hemangioma Esplénico no Adulto e Síndrome de Kasabach-Merritt

Abstract

The Kasabach Merritt syndrome is a rare disease that is characteristic of youth ages, that counts as an association of capillary hemangioma and thrombocytopenia. We present a rare case of a 65 years old male patient, followed in outpatient hematology clinic for abdominal mass, thrombocytopenia and coagulopathy. Clinical research has revealed a large hemangioma occupying almost the entire splenic parenchyma. He underwent total splenectomy, checking the subsequent correction of thrombocytopenia. We present this case because of the rarity of the association between splenic cavernous hemangioma and this syndrome, emphasizing the contribution of surgical treatment and iconographic documentation collected.

Keywords: hemangioma; splenic neoplasm; Kasabach Merritt syndrome, splenectomy.