CAROLI’S DISEASE IN ADULTHOOD – A CASE REPORT

Abstract





Caroli’s disease (CD) is a rare congenital disorder defined by multifocal segmental dilatation of intrahepatic bile ducts. It may cause severe, life-threatening cholangitis hepatobiliary degeneration or even cancer. A 63-years-old male with monolobar CD managed with conservative treatment is presented with revision of literature. The patient presented in the emergency department with a six-hour history of cholic epigastric pain with dorsal irradiation and a normal physical exam. Past medical history included colonic polyposis, Chronic Obstructive Pulmonary Disease (COPD) and Benign Prostatic Hyperplasia. Investigation revealed infracentimetric left cystic dilatation of intrahepatic bile ducts suggestive of Caroli’s disease. Despite its rare incidence, CD should be considered in patients with recurrent cholangitis. The diagnosis of CD relies mostly on imaging studies. Treatment should be customized and multi-disciplinary.





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References

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Published
2023-06-23
How to Cite
FERNANDES, Urânia et al. CAROLI’S DISEASE IN ADULTHOOD – A CASE REPORT. Revista Portuguesa de Cirurgia, [S.l.], n. 55, p. 28-31, june 2023. ISSN 2183-1165. Available at: <https://revista.spcir.com/index.php/spcir/article/view/877>. Date accessed: 17 june 2024. doi: https://doi.org/10.34635/rpc.877.
Section
Clinical Case