Caroli`s Disease: surgical treatment, hepatic ressection and transplantation in seven years

  • A. Bento Interno de Cirurgia Geral, Hospitais da Universidade de Coimbra, Portugal
  • C. Pinheiro Interno de Cirurgia Geral, Hospitais da Universidade de Coimbra, Portugal
  • H. Baptista Assistente Graduado de Cirurgia Geral, Hospitais da Universidade de Coimbra, Portugal
  • M. Silva Assistente Graduado de Anatomia Patológica, Hospitais da Universidade de Coimbra, Portugal
  • E. Furtado Assistente Graduado de Cirurgia Geral, Hospitais da Universidade de Coimbra, Portugal
  • F. Martinho Director de Serviço de Cirurgia Geral, Hospitais da Universidade de Coimbra, Portugal

Abstract

Objectives: We review seven years of experience of surgical treatment of CD (Caroli Disease) in the HUC (Hospitais da Unversidade de Coimbra).

Material and methods: Histopathology records from July 2000 to July 2007 were scanned CD. Patient files were retrieved and reviewed for demographic and clinical data, comorbidity and exam results. Previous diagnosis, medical treatments and other data pertaining to congenital biliary tree malformations were sought.

Results: Between July 2000 and July 2007, eight patients with histologically confirmed CD were treated in the HUC. The average age was 41,2 years. Seven patients have a history of previous cholangitis. Six patients had hepatic resection and the remaining two had liver transplantation. At present all eight patients are alive and experience clinical improvement.

Conclusion: Hepatic resection is the choice treatment for localized CD, and it is potentially curative. However, for diffuse disease liver transplant may be the only option, and it may provide good long term results.

Keywords: Caroli disease; biliar tree dilation; cholangitis 

Downloads

Download data is not yet available.
Published
2008-09-27
How to Cite
BENTO, A. et al. Caroli`s Disease: surgical treatment, hepatic ressection and transplantation in seven years. Revista Portuguesa de Cirurgia, [S.l.], n. 6, p. 9-15, sep. 2008. ISSN 2183-1165. Available at: <https://revista.spcir.com/index.php/spcir/article/view/243>. Date accessed: 28 mar. 2024.
Section
Original Papers