Angiomyolipoma is a rare benign mesenchymal tumor. Usually located in the kidney, with an incidence of 0.3-3%. Extra-renal angiomyolipomas are extremely rare, with not much more than fifty cases having been described.
We report a case of a healthy 50 year-old man, who presented with episodes of melena. Routine blood tests showed a hypochromic and microcytic anemia. An endoscopy showed an extrinsic lesion compressing the transition of the gastric body and antrum. A CT-scan of the abdomen revealed an intraluminal pedunculated tumor that originated in the third part of the duodenum and extended to the Treitz region.
The patient underwent to a laparotomy with duodenotomy and excision of the pedunculated tumor. Histopathological examination revealed an angiomyolipoma.
There appears to be only one previous report of duodenal angiomyolipoma in the literature.
Keywords: Angiomyolipoma; duodenum; mesenchymal tumor